Orderable Name PUPYP Purines and Pyrimidines Panel, Plasma
Ordering Guidance
The preferred test to rule-out inherited disorders of purine and pyrimidine metabolism is PUPYU / Purines and Pyrimidines Panel, Random, Urine.
This test does not evaluate succinyladenosine. If succinyladenosine analysis is needed, order PUPYU / Purines and Pyrimidines Panel, Random, Urine.
Necessary Information
Patient's age is required.
Specimen Required
Collection Container/Tube: Lavender top (EDTA)
Submission Container/Tube: Plastic vial
Specimen Volume: 0.5 mL
Collection Instructions:
1. Centrifuge at 4° C and aliquot plasma into plastic vial.
2. Send plasma frozen.
Useful For
Evaluating patients with symptoms suspicious for disorders of purine and pyrimidine metabolism
Monitoring patients with disorders of purine and pyrimidine metabolism
Laboratory evaluation of primary and secondary hyperuricemias
Assessing tolerance for fluoropyrimidine drugs used in cancer treatment
Aiding in the diagnosis of individuals with suspected dihydropyrimidine dehydrogenase deficiency
Special Instructions
Method Name
Liquid Chromatography Tandem Mass Spectrometry (LC-MS/MS)
Specimen Type
PlasmaSpecimen Minimum Volume
0.2 mL
Specimen Stability Information
Specimen Type | Temperature | Time | Special Container |
---|---|---|---|
Plasma | Frozen | 90 days |
Reject Due To
Gross hemolysis | OK |
Gross lipemia | OK |
Gross icterus | OK |
Reference Values
Age range |
0-1 years |
>1-4 years |
5-18 years |
>18 years |
Uracil |
≤2 |
≤2 |
≤2 |
≤2 |
Thymine |
≤2 |
≤2 |
≤2 |
≤2 |
Adenine |
≤3 |
≤3 |
≤3 |
≤3 |
Hypoxanthine |
≤35 |
≤17 |
≤15 |
≤15 |
Xanthine |
≤6 |
≤6 |
≤6 |
≤3 |
Dihydroorotic |
≤2 |
≤2 |
≤2 |
≤2 |
Uric Acid |
100-450 |
150-500 |
150-500 |
150-500 |
Deoxythymidine |
≤2 |
≤2 |
≤2 |
≤2 |
Deoxyuridine |
≤2 |
≤2 |
≤2 |
≤2 |
Uridine |
≤14 |
≤9 |
≤9 |
≤9 |
Deoxyinosine |
≤2 |
≤2 |
≤2 |
≤2 |
Deoxyguanosine |
≤2 |
≤2 |
≤2 |
≤2 |
Inosine |
≤2 |
≤2 |
≤2 |
≤2 |
Guanosine |
≤2 |
≤2 |
≤2 |
≤2 |
Dihydrouracil |
≤3 |
≤3 |
≤3 |
≤3 |
Dihydrothymine |
≤2 |
≤2 |
≤2 |
≤2 |
N-carbamoyl- beta-alanine |
≤2 |
≤2 |
≤2 |
≤2 |
N-carbamoyl- beta-aminoisobutryic acid |
≤2 |
≤2 |
≤2 |
≤2 |
All results reported as nmol/mL
Day(s) Performed
Tuesday
Report Available
3 to 9 daysCPT Code Information
82542
Testing Algorithm
For information see: Epilepsy: Unexplained Refractory and/or Familial Testing Algorithm.
Forms
If not ordering electronically, complete, print, and send a Biochemical Genetics Test Request (T798) with the specimen.